Lung Transplantation for Pleuroparenchymal Fibroelastosis


This retrospective observational study will evaluate the outcomes of lung transplantation for a rare cause of interstitial lung disease called pleuroparenchymal fibroelastosis. Data will be collected from all transplantation center in France.

Full Title of Study: “Lung Transplantation for Pleuroparenchymal Fibroelastosis : a French Multicentric Retrospective Study”

Study Type

  • Study Type: Observational
  • Study Design
    • Time Perspective: Retrospective
  • Study Primary Completion Date: July 1, 2021


  • Procedure: Lung transplantation (single, lobar or bilateral lung transplantation)
    • Lung transplantation were performed for end-stage interstitial lung disease secondary to pleuroparenchymal fibroelastosis

Arms, Groups and Cohorts

  • lung transplantation
    • Lung transplantation performed for end-stage interstitial lung disease secondary to pleuroparenchymal fibroelastosis.

Clinical Trial Outcome Measures

Primary Measures

  • Post-operative mortality
    • Time Frame: Any death up to 90 days after lung transplantation
    • Any death after lung transplantation during the first 30 days or during the hospitalization following the lung transplantation (in-hospital mortality)

Participating in This Clinical Trial

Inclusion Criteria

  • Lung transplantation (any type) for pleuroparenchymal fibroelastosis – Histologically confirmed pleuroparenchymal fibroelastosis on the recipient lungs Exclusion Criteria:

  • All other interstitial lung disease than pleuroparenchymal fibroelastosis – Pleuroparenchymal fibroelastosis who didn't underwent lung transplantation

Gender Eligibility: All

Minimum Age: N/A

Maximum Age: N/A

Are Healthy Volunteers Accepted: No

Investigator Details

  • Lead Sponsor
    • Hospices Civils de Lyon
  • Provider of Information About this Clinical Study
    • Sponsor

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